Perivascular epithelioid cell tumor (PEComa) of the uterus with aggressive behavior at presentation
نویسندگان
چکیده
منابع مشابه
Perivascular epithelioid cell tumor (PEComa) in the genitourinary tract.
Perivascular epithelioid cell tumors (PEComas) are mesenchymal tumors composed of histologically, immunohistochemically, ultrastructurally, and genetically distinctive cells. PEComas have been described in different organs and are considered ubiquitous tumors. In this review we discuss recent informations related to PEComas in the genitourinary tract.
متن کاملPigmented perivascular epithelioid cell tumor (PEComa) arising from kidney
INTRODUCTION Perivascular epithelioid cell tumor (PEComa) is a mesenchymal neoplasm composed of perivascular epithelioid cells with clear to eosinophilic cytoplasm. Pigmented PEComa arising from kidney is extraordinarily rare and sometimes can exhibit aggressive biological behavior. CASE REPORT We present here a rare case of pigmented renal PEComa in a 46-year-old female. The patient had comp...
متن کاملMalignant perivascular epithelioid cell tumor of the uterus
Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non-classic anatomic distributions are known as perivascular epithelioid cell tumor-not otherwise specified (PEComa-NOS), and one of the most common primary sites for PEComa-NOS is the uterus. The ris...
متن کاملPerivascular epithelioid tumor (PEComa) of the falciform/ broad ligament.
PEComas localized in the region of falciform ligament and broad ligament are exceedingly rare. Most of them are built of spindle neoplastic cells. We report a case of epithelioid PEComa of the falciform ligament and/or broad ligament. There is only one report of such neoplasm in English-language literature. Histologically, the tumor was composed of nests of epithelioid clear cells stained posit...
متن کاملPerivascular epithelioid cell tumor (PEComa) of the urinary bladder associated with Xp11 translocation.
Perivascular epithelioid cell-containing tumors (PEComas) represent a rare family of neoplasms. Their dichotomous phenotypic features, including both myogenic and mylanocytic features, can make a definitive diagnosis difficult. Such tumors have been associated with the overexpression of transcription factor E3 (TFE3). An Xp11 translocation could account for the aberrant activity of TFE3 but has...
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ژورنال
عنوان ژورنال: Hematology/Oncology and Stem Cell Therapy
سال: 2009
ISSN: 1658-3876
DOI: 10.1016/s1658-3876(09)50013-1